Panniculitis-like T-cell-lymphoma in the mesentery associated with hemophagocytic syndrome: autopsy case report
The result's identifiers
Result code in IS VaVaI
<a href="https://www.isvavai.cz/riv?ss=detail&h=RIV%2F00064173%3A_____%2F19%3AN0000018" target="_blank" >RIV/00064173:_____/19:N0000018 - isvavai.cz</a>
Alternative codes found
RIV/00216208:11120/19:43918470 RIV/00216208:11130/19:10395705 RIV/00064203:_____/19:10395705
Result on the web
<a href="https://doi.org/10.1186/s13000-019-0854-9" target="_blank" >https://doi.org/10.1186/s13000-019-0854-9</a>
DOI - Digital Object Identifier
<a href="http://dx.doi.org/10.1186/s13000-019-0854-9" target="_blank" >10.1186/s13000-019-0854-9</a>
Alternative languages
Result language
angličtina
Original language name
Panniculitis-like T-cell-lymphoma in the mesentery associated with hemophagocytic syndrome: autopsy case report
Original language description
BACKGROUND: Panniculitis-like T-cell lymphoma is an uncommon type of non-Hodgkin lymphoma, occurring usually in the form of nodules within the subcutaneous fat tissue of the extremities or trunk. In the literature, subcutaneous panniculitis-like T-cell lymphoma (SPTCL) is described as a distinct type of T-cell lymphoma with a variable clinical behavior, depending on molecular phenotype of T-cell receptor (TCR) and on the presence or absence of hemophagocytic syndrome. CASE PRESENTATION: We present a bioptic and autoptic case of a 65-years old Caucasian man with panniculitic T-cell lymphoma with morphological and immunohistochemical features of SPTCL, limited to the retroperitoneal and mesenteric mass, i.e. without any cutaneous involvement, and associated with severe hemophagocytic lymphohistiocytosis. CONCLUSION: A panniculitic T-cell lymphoma with morphological and molecular features of SPTCL, which is limited to mesentery, i.e. does not involve subcutaneous fat, seems to be exceedingly rare.
Czech name
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Czech description
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Classification
Type
J<sub>imp</sub> - Article in a specialist periodical, which is included in the Web of Science database
CEP classification
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OECD FORD branch
30109 - Pathology
Result continuities
Project
—
Continuities
I - Institucionalni podpora na dlouhodoby koncepcni rozvoj vyzkumne organizace
Others
Publication year
2019
Confidentiality
S - Úplné a pravdivé údaje o projektu nepodléhají ochraně podle zvláštních právních předpisů
Data specific for result type
Name of the periodical
Diagnostic Pathology
ISSN
1746-1596
e-ISSN
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Volume of the periodical
14
Issue of the periodical within the volume
July
Country of publishing house
GB - UNITED KINGDOM
Number of pages
7
Pages from-to
80
UT code for WoS article
000475789400002
EID of the result in the Scopus database
2-s2.0-85069448768