Aortic dissection and rupture in a 16-year-old girl with Turner syndrome following previous progression of aortic dilation

Result code in IS VaVaI

<a href="https://www.isvavai.cz/riv?ss=detail&h=RIV%2F00064203%3A_____%2F10%3A6293" target="_blank" >RIV/00064203:_____/10:6293 - isvavai.cz</a>

Alternative codes found

RIV/00216208:11130/10:6293

Result on the web

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DOI - Digital Object Identifier

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Result language

angličtina

Original language name

Aortic dissection and rupture in a 16-year-old girl with Turner syndrome following previous progression of aortic dilation

Original language description

Aortic dissection occurs in Turner syndrome with substantially higher frequency in comparison to the general population, and its prevention is one of the main aims of cardiologic follow-up. Findings of cystic medial necrosis in the aortic wall and a highprevalence of aortic dilation suggest that a form of aortopathy exists in Turner syndrome. However, little is known about natural development of aortic dilation prior to dissection. We present a 16-year-old girl with Turner syndrome with a bicuspid aortic valve, aortic stenosis, and dilation of ascending aorta, who underwent annual echocardiographic examinations from early childhood. Significant progressions of proximal aortic dilation occurred twice at the age of 10 and 15 years. Thereafter, another rapid progression was observed during 8 months and within 3 weeks preceding dissection. Acute aortic dissection was diagnosed while the girl was waiting for elective surgery. She was successfully operated. Frequent estimations of aortic di

Czech name

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Czech description

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Type

J_x - Unclassified - Peer-reviewed scientific article (Jimp, Jsc and Jost)

CEP classification

FG - Paediatrics

OECD FORD branch

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Project

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Continuities

Z - Vyzkumny zamer (s odkazem do CEZ)

Publication year

2010

Confidentiality

S - Úplné a pravdivé údaje o projektu nepodléhají ochraně podle zvláštních právních předpisů

Name of the periodical

European Journal of Pediatrics

ISSN

0340-6199

e-ISSN

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Volume of the periodical

169

Issue of the periodical within the volume

10

Country of publishing house

DE - GERMANY

Number of pages

4

Pages from-to

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UT code for WoS article

000281238700019

EID of the result in the Scopus database

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