Idiopathic vs. secondary retroperitoneal fibrosis: a clinicopathological study of 12 cases, with emphasis to possible relationship to IgG4-related disease

Result code in IS VaVaI
<a href="https://www.isvavai.cz/riv?ss=detail&h=RIV%2F00179906%3A_____%2F13%3A10173407" target="_blank" >RIV/00179906:_____/13:10173407 - isvavai.cz</a>
Alternative codes found
RIV/00216208:11150/13:10173407
Result on the web
<a href="http://download.springer.com/static/pdf/855/art%253A10.1007%252Fs00428-013-1480-7.pdf?auth66=1392201175_27eff28118401c974372fc078e55ee3d&ext=.pdf" target="_blank" >http://download.springer.com/static/pdf/855/art%253A10.1007%252Fs00428-013-1480-7.pdf?auth66=1392201175_27eff28118401c974372fc078e55ee3d&ext=.pdf</a>
DOI - Digital Object Identifier
<a href="http://dx.doi.org/10.1007/s00428-013-1480-7" target="_blank" >10.1007/s00428-013-1480-7</a>

Result language
angličtina
Original language name
Idiopathic vs. secondary retroperitoneal fibrosis: a clinicopathological study of 12 cases, with emphasis to possible relationship to IgG4-related disease
Original language description
Retroperitoneal fibrosis (RF) is a rare disease characterized by inflammation and fibrosis of retroperitoneal soft tissues. It is classified into 2 types: idiopathic (iRF), and secondary (sRF). The aim of the study was to investigate the relationship between iRF and IgG4-related disease (IgG4-RD) and to eventually extend the clinicopathological features of this condition by analysis of the sample comprising 6 iRF- and 6 sRF-patients. The iRF-patients included 4 males and 2 females, aged 12-62 years (median 55 years). Two lesions were periaortic, 1 was periureteral and 3 cases showed both periaortic and periureteral localization. Two patients had increased serum levels of IgG4. None of the patients developed any manifestation of IgG4-RD during the follow-up period ranging for 15 - 133 months (median 43 months). Microscopically, in 2 iRF-cases fibrosis was highly cellular encircling vessels, nerves and paraganglia. Phlebitis was found in all cases being obliterative in 4. Lymphocytic inf
Czech name
—
Czech description
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Type
J<sub>x</sub> - Unclassified - Peer-reviewed scientific article (Jimp, Jsc and Jost)
CEP classification
FP - Other medical fields
OECD FORD branch
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Project
<a href="/en/project/LM2010004" target="_blank" >LM2010004: BBMRI_CZ in the building of the Czech part of a large distributed research infrastructure of pan-European importance: the creation and operation of the network of banks of biological material for biomedical research</a><br>
Continuities
I - Institucionalni podpora na dlouhodoby koncepcni rozvoj vyzkumne organizace

Publication year
2013
Confidentiality
S - Úplné a pravdivé údaje o projektu nepodléhají ochraně podle zvláštních právních předpisů

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