Stewart-Treves syndrome: Case report and literature review

Result code in IS VaVaI

<a href="https://www.isvavai.cz/riv?ss=detail&h=RIV%2F00216208%3A11140%2F20%3A10415890" target="_blank" >RIV/00216208:11140/20:10415890 - isvavai.cz</a>

Alternative codes found

RIV/00669806:_____/20:10415890

Result on the web

<a href="https://verso.is.cuni.cz/pub/verso.fpl?fname=obd_publikace_handle&handle=Y8qXADpBbQ" target="_blank" >https://verso.is.cuni.cz/pub/verso.fpl?fname=obd_publikace_handle&handle=Y8qXADpBbQ</a>

DOI - Digital Object Identifier

<a href="http://dx.doi.org/10.1016/j.rpor.2020.09.006" target="_blank" >10.1016/j.rpor.2020.09.006</a>

Result language

angličtina

Original language name

Stewart-Treves syndrome: Case report and literature review

Original language description

tLymphangiosarcoma, or Stewart-Treves Syndrome (STS), is a very rare skin angiosarcoma with poor prog-nosis, which usually affects the upper limbs of patients who underwent breast cancer surgery, includingaxillary dissection followed by radiotherapy (RT). Cutaneous lymphangiosarcomas, which account forapproximately 5% of all angiosarcomas, usually originate in the limb with chronic lymphedema. Lym-phatic blockade is involved in the onset of STS. RT contributes indirectly to an increased risk of developingSTS by causing axillary-node sclerosis and resulting in a lymphatic blockade and lymphedema. Chroniclymphedema causes local immunodeficiency, which indirectly leads to oncogenesis. Currently, axillarynodes are no longer routinely irradiated after axillary dissection, which is associated with a reduction inthe incidence of chronic lymphedema from 40% to 4%. The use of sentinel lymph node biopsy techniqueis also widespread and the associated risk of lymphedema is further reduced. Thus, the incidence of STSdecreased significantly with improved surgical and radiation techniques. The overall prognosis of STSpatients is very poor. Only early radical surgical removal, including amputation or disarticulation of theaffected limb, or wide excision at an early stage offers the greatest chance of long-term survival. Only afew case reports and series with a small number of patients with lymphangiosarcoma can be found in theliterature. We present a case report of the first diagnosed STS at our department in an effort to highlightthe need of the consideration of developing lymphangiosarcoma in patients with chronic lymphedema.

Czech name

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Czech description

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Type

J_imp - Article in a specialist periodical, which is included in the Web of Science database

CEP classification

—

OECD FORD branch

30204 - Oncology

Project

—

Continuities

I - Institucionalni podpora na dlouhodoby koncepcni rozvoj vyzkumne organizace

Publication year

2020

Confidentiality

S - Úplné a pravdivé údaje o projektu nepodléhají ochraně podle zvláštních právních předpisů

Name of the periodical

Reports of Practical Oncology and Radiotherapy

ISSN

1507-1367

e-ISSN

—

Volume of the periodical

25

Issue of the periodical within the volume

6

Country of publishing house

PL - POLAND

Number of pages

5

Pages from-to

934-938

UT code for WoS article

000604399200015

EID of the result in the Scopus database

2-s2.0-85092140882