The Association of methylprednisolone dosing to cessation of myotonia in a patient with myotonic dystrophy type 1

Result code in IS VaVaI

<a href="https://www.isvavai.cz/riv?ss=detail&h=RIV%2F00216224%3A14110%2F20%3A00115973" target="_blank" >RIV/00216224:14110/20:00115973 - isvavai.cz</a>

Alternative codes found

RIV/65269705:_____/20:00072811

Result on the web

<a href="https://www.sciencedirect.com/science/article/pii/S0960896620300663?via%3Dihub" target="_blank" >https://www.sciencedirect.com/science/article/pii/S0960896620300663?via%3Dihub</a>

DOI - Digital Object Identifier

<a href="http://dx.doi.org/10.1016/j.nmd.2020.03.004" target="_blank" >10.1016/j.nmd.2020.03.004</a>

Result language

angličtina

Original language name

The Association of methylprednisolone dosing to cessation of myotonia in a patient with myotonic dystrophy type 1

Original language description

We report the case of a patient suffering from duplicity of myotonic dystrophy type 1 and ulcerative colitis whose treatment for ulcerative colitis included repeated administrations of descending doses of methylprednisolone and in whom we found an association between methylprednisolone dosing and cessation of myotonia. Myotonia severity was expressed as relaxation time after voluntary contraction and as a patient-reported outcome using the Czech version of the Myotonia Behavior Scale. The patient was being treated for a flare of ulcerative colitis, starting with 32 mg of methylprednisolone and reducing the dose by 4 mg a week. The symptoms of myotonia began to wear off three weeks after starting methylprednisolone and had totally disappeared by four weeks after starting methylprednisolone. The first symptoms of myotonia returned about a month after the last dose of methylprednisolone and reached a peak of severity more than two months after the final dose. (C) 2020 Elsevier B.V. All rights reserved.

Czech name

—

Czech description

—

Type

J_imp - Article in a specialist periodical, which is included in the Web of Science database

CEP classification

—

OECD FORD branch

30103 - Neurosciences (including psychophysiology)

Project

—

Continuities

S - Specificky vyzkum na vysokych skolach

Publication year

2020

Confidentiality

S - Úplné a pravdivé údaje o projektu nepodléhají ochraně podle zvláštních právních předpisů

Name of the periodical

Neuromuscular Disorders

ISSN

0960-8966

e-ISSN

1873-2364

Volume of the periodical

30

Issue of the periodical within the volume

5

Country of publishing house

GB - UNITED KINGDOM

Number of pages

4

Pages from-to

427-430

UT code for WoS article

000539369800009

EID of the result in the Scopus database

2-s2.0-85083312575