Desmoplastic Small Round Cell Tumor as a Rare Cause of an Incarcerated Epigastric Linea Alba Hernia: A Case Report and Literature Review
The result's identifiers
Result code in IS VaVaI
<a href="https://www.isvavai.cz/riv?ss=detail&h=RIV%2F00216224%3A14110%2F24%3A00136141" target="_blank" >RIV/00216224:14110/24:00136141 - isvavai.cz</a>
Result on the web
<a href="https://www.cureus.com/articles/260497-desmoplastic-small-round-cell-tumor-as-a-rare-cause-of-an-incarcerated-epigastric-linea-alba-hernia-a-case-report-and-literature-review#!/" target="_blank" >https://www.cureus.com/articles/260497-desmoplastic-small-round-cell-tumor-as-a-rare-cause-of-an-incarcerated-epigastric-linea-alba-hernia-a-case-report-and-literature-review#!/</a>
DOI - Digital Object Identifier
<a href="http://dx.doi.org/10.7759/cureus.61729" target="_blank" >10.7759/cureus.61729</a>
Alternative languages
Result language
angličtina
Original language name
Desmoplastic Small Round Cell Tumor as a Rare Cause of an Incarcerated Epigastric Linea Alba Hernia: A Case Report and Literature Review
Original language description
Desmoplastic small round cell tumor is a very rare soft tissue sarcoma with a bleak prognosis and short patient survival. The most common occurrence is in 20-30-year-old men. Our study presents the case report of a 40-year-old patient who was diagnosed with this sarcoma. The first symptom of the illness was an incarcerated epigastric hernia with sarcoma metastasis resembling an intestinal loop in an ultrasound image. The fluorescence in situ hybridization (FISH) method showed a fusion of the EWS and WT1 genes. Systemic palliative chemotherapy using the VDC-IE (vincristine, doxorubicin, cyclophosphamide, ifosfamide, and etoposide) regimen was chosen instead of further surgery due to the disease's generalization. However, the therapy failed to halt the disease progression and was thus terminated after 18 months. The patient's overall survival was 19 months. The rare character of this disease complicates the diagnostics in clinical practice. Nevertheless, rare sarcomas should be considered in patients with non-specific abdominal symptoms, including patients with incarcerated ventral hernia.
Czech name
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Czech description
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Classification
Type
J<sub>imp</sub> - Article in a specialist periodical, which is included in the Web of Science database
CEP classification
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OECD FORD branch
30204 - Oncology
Result continuities
Project
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Continuities
S - Specificky vyzkum na vysokych skolach
Others
Publication year
2024
Confidentiality
S - Úplné a pravdivé údaje o projektu nepodléhají ochraně podle zvláštních právních předpisů
Data specific for result type
Name of the periodical
CUREUS
ISSN
2168-8184
e-ISSN
2168-8184
Volume of the periodical
16
Issue of the periodical within the volume
6
Country of publishing house
US - UNITED STATES
Number of pages
7
Pages from-to
1-7
UT code for WoS article
001259101000034
EID of the result in the Scopus database
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