European principles of inhibitor management in patients with haemophilia

Result code in IS VaVaI

<a href="https://www.isvavai.cz/riv?ss=detail&h=RIV%2F65269705%3A_____%2F18%3A00069286" target="_blank" >RIV/65269705:_____/18:00069286 - isvavai.cz</a>

Result on the web

<a href="https://ojrd.biomedcentral.com/articles/10.1186/s13023-018-0800-z" target="_blank" >https://ojrd.biomedcentral.com/articles/10.1186/s13023-018-0800-z</a>

DOI - Digital Object Identifier

<a href="http://dx.doi.org/10.1186/s13023-018-0800-z" target="_blank" >10.1186/s13023-018-0800-z</a>

Result language

angličtina

Original language name

European principles of inhibitor management in patients with haemophilia

Original language description

Background: In spite of recent major advances in the understanding and treatment of inhibitor development in patients with haemophilia, multidisciplinary management of many of these patients remains suboptimal and highly heterogenous across Europe. Methods: Following a series of multidisciplinary meetings and a review of the literature, the European haemophilia community of health professionals and patients jointly defined practical optimum standards for ensuring and harmonizing treatment and care for patients with an inhibitor. Results: Ten complementary principles for the management of inhibitors in haemophilia have been developed, emphasizing the importance and benefits of a centralized, multidisciplinary, expert and holistic approach. Conclusions: This document will serve as a benchmark to improve the multidisciplinary and practical management of patients with inhibitor. Implementation and adherence to each of these principles should have a major positive impact on the management and outcomes of patients developing an inhibitor.

Czech name

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Czech description

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Type

J_imp - Article in a specialist periodical, which is included in the Web of Science database

CEP classification

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OECD FORD branch

30101 - Human genetics

Project

—

Continuities

I - Institucionalni podpora na dlouhodoby koncepcni rozvoj vyzkumne organizace

Publication year

2018

Confidentiality

S - Úplné a pravdivé údaje o projektu nepodléhají ochraně podle zvláštních právních předpisů

Name of the periodical

Orphanet Journal of Rare Diseases

ISSN

1750-1172

e-ISSN

—

Volume of the periodical

13

Issue of the periodical within the volume

APR 2018

Country of publishing house

GB - UNITED KINGDOM

Number of pages

6

Pages from-to

66

UT code for WoS article

000431528600001

EID of the result in the Scopus database

2-s2.0-85046255948