Ebstein's anomaly with significant dysplasia of the tricuspid valve presenting at 73 years of age. A case report
The result's identifiers
Result code in IS VaVaI
<a href="https://www.isvavai.cz/riv?ss=detail&h=RIV%2F65269705%3A_____%2F19%3A00070950" target="_blank" >RIV/65269705:_____/19:00070950 - isvavai.cz</a>
Alternative codes found
RIV/00216224:14110/19:00112953
Result on the web
<a href="https://e-coretvasa.cz/pdfs/cor/2019/03/10.pdf" target="_blank" >https://e-coretvasa.cz/pdfs/cor/2019/03/10.pdf</a>
DOI - Digital Object Identifier
<a href="http://dx.doi.org/10.1016/j.crvasa.2018.07.004" target="_blank" >10.1016/j.crvasa.2018.07.004</a>
Alternative languages
Result language
angličtina
Original language name
Ebstein's anomaly with significant dysplasia of the tricuspid valve presenting at 73 years of age. A case report
Original language description
Ebstein's anomaly (EA) is a rare congenital heart defect, characterized by an anomalous tricuspid valve displaced towards the apex of the right ventricle (RV); it is usually accompanied by regurgitation. While its severe forms with an extremely dilated functional RV and oppression of the left heart chambers result in the development of severe heart failure at a young age and, in some cases, even prenatally, patients with mild EA may live until old age with the condition unrecognized. We present the case of a patient with a milder form of EA and a contribution of dysplasia, with the disease undiagnosed until his eighties when he developed heart failure accompanied by significant tricuspid regurgitation. Tricuspid valve replacement with a bioprosthesis and atrial septal defect occlusion were followed by significant improvement of RV function and remission of the patient's problems.
Czech name
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Czech description
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Classification
Type
J<sub>imp</sub> - Article in a specialist periodical, which is included in the Web of Science database
CEP classification
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OECD FORD branch
30201 - Cardiac and Cardiovascular systems
Result continuities
Project
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Continuities
I - Institucionalni podpora na dlouhodoby koncepcni rozvoj vyzkumne organizace
Others
Publication year
2019
Confidentiality
S - Úplné a pravdivé údaje o projektu nepodléhají ochraně podle zvláštních právních předpisů
Data specific for result type
Name of the periodical
Cor et Vasa
ISSN
0010-8650
e-ISSN
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Volume of the periodical
61
Issue of the periodical within the volume
3
Country of publishing house
NL - THE KINGDOM OF THE NETHERLANDS
Number of pages
4
Pages from-to
314-317
UT code for WoS article
000472526800010
EID of the result in the Scopus database
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