Thrombotic thrombocytopenic purpura : incidence of congenital form of disease in North Moravia (region Moravia-Silesia)

Result code in IS VaVaI

<a href="https://www.isvavai.cz/riv?ss=detail&h=RIV%2F00023736%3A_____%2F09%3A00008263" target="_blank" >RIV/00023736:_____/09:00008263 - isvavai.cz</a>

Alternative codes found

RIV/61988987:17110/09:A1000WXE RIV/00843989:_____/09:00100846

Result on the web

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DOI - Digital Object Identifier

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Result language

angličtina

Original language name

Thrombotic thrombocytopenic purpura : incidence of congenital form of disease in North Moravia (region Moravia-Silesia)

Original language description

Thrombotic thrombocytopenic purpura (TTP) was first described by Eli Moschcowitz in 1924. The pathophysiology of this disease is related to unusual, large multimers of von Willebrand factor in microcirculation, that are insufficiently cleaved by ADAMTS13protease (a disintegrin-like and metalloprotease with thrombospondin type 1motif,13). Congenital TTP/Upshaw-Schulman syndrome is less frequent than acquired one TTP/HUS (haemolytic-ureamic syndrome). Short characteristic of patients with inherited formof TTP is reported as well as their clinical and laboratory features and management of treatment.

Czech name

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Czech description

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Type

J_x - Unclassified - Peer-reviewed scientific article (Jimp, Jsc and Jost)

CEP classification

FD - Oncology and haematology

OECD FORD branch

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Project

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Continuities

V - Vyzkumna aktivita podporovana z jinych verejnych zdroju

Publication year

2009

Confidentiality

S - Úplné a pravdivé údaje o projektu nepodléhají ochraně podle zvláštních právních předpisů

Name of the periodical

Prague Medical Report (dříve Sborník lékařský)

ISSN

1214-6994

e-ISSN

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Volume of the periodical

110

Issue of the periodical within the volume

3

Country of publishing house

CZ - CZECH REPUBLIC

Number of pages

6

Pages from-to

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UT code for WoS article

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EID of the result in the Scopus database

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