Primary ciliary dyskinesia: a consensus statement on diagnostic and treatment approaches in children

Result code in IS VaVaI
<a href="https://www.isvavai.cz/riv?ss=detail&h=RIV%2F00064203%3A_____%2F09%3A5728" target="_blank" >RIV/00064203:_____/09:5728 - isvavai.cz</a>
Alternative codes found
RIV/00216208:11130/09:5728
Result on the web
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DOI - Digital Object Identifier
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Result language
angličtina
Original language name
Primary ciliary dyskinesia: a consensus statement on diagnostic and treatment approaches in children
Original language description
Primary ciliary dyskinesia (PCD) is associated with abnormal ciliary structure and function, resulting in retention of mucus and bacteria in the respiratory tract, leading to chronic oto-sino-pulmonary disease, situs abnormalities and abnormal sperm motility. The diagnosis of PCD requires presence of the characteristic clinical phenotype and either specific ultrastructural ciliary defects identified by electron microscopy or evidence of abnormal ciliary function. Although the management of children withPCD remains uncertain and evidence is limited, it remains important to follow-up these patients with an adequate and shared care system in order to prevent future lung damage. This ERS consensus statement on the management of children with PCD formulates recommendations for diagnostic and therapeutic approaches with more accurate approach in these patients. Large well-designed randomised controlled trials are required to improve these recommendations.
Czech name
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Czech description
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Type
J<sub>x</sub> - Unclassified - Peer-reviewed scientific article (Jimp, Jsc and Jost)
CEP classification
FC - Pneumology
OECD FORD branch
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Publication year
2009
Confidentiality
S - Úplné a pravdivé údaje o projektu nepodléhají ochraně podle zvláštních právních předpisů

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