Management of primary ciliary dyskinesia in European children: recommendations and clinical practice

Result code in IS VaVaI
<a href="https://www.isvavai.cz/riv?ss=detail&h=RIV%2F00064203%3A_____%2F12%3A8108" target="_blank" >RIV/00064203:_____/12:8108 - isvavai.cz</a>
Alternative codes found
RIV/00216208:11130/12:8108
Result on the web
<a href="http://dx.doi.org/10.1183/09031936.00073911" target="_blank" >http://dx.doi.org/10.1183/09031936.00073911</a>
DOI - Digital Object Identifier
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Result language
angličtina
Original language name
Management of primary ciliary dyskinesia in European children: recommendations and clinical practice
Original language description
The European Respiratory Society Task Force on primary ciliary dyskinesia (PCD) in children recently published recommendations for diagnosis and management. This paper compares these recommendations with current clinical practice in Europe. Questionnaires were returned by 194 paediatric respiratory centres caring for PCD patients in 26 countries. In most countries, PCD care was not centralised, with a median (interquartile range) of 4 (2-9) patients treated per centre. Overall, 90% of centres had accessto nasal or bronchial mucosa! biopsy. Samples were analysed by electron microscopy (77%) and ciliary function tests (57%). Nasal nitric oxide was used for screening in 46% of centres and saccharine tests in 36%. Treatment approaches varied widely, bothwithin and between countries. European region, size of centre and the country's general government expenditure on health partly defined availability of advanced diagnostic tests and choice of treatments. In conclusion, we found substantia
Czech name
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Czech description
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Type
J<sub>x</sub> - Unclassified - Peer-reviewed scientific article (Jimp, Jsc and Jost)
CEP classification
FC - Pneumology
OECD FORD branch
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Publication year
2012
Confidentiality
S - Úplné a pravdivé údaje o projektu nepodléhají ochraně podle zvláštních právních předpisů

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