Towards a new set of classification criteria for PFAPA syndrome
The result's identifiers
Result code in IS VaVaI
<a href="https://www.isvavai.cz/riv?ss=detail&h=RIV%2F00216208%3A11110%2F18%3A10381871" target="_blank" >RIV/00216208:11110/18:10381871 - isvavai.cz</a>
Alternative codes found
RIV/00064165:_____/18:10381871
Result on the web
<a href="https://doi.org/10.1186/s12969-018-0277-2" target="_blank" >https://doi.org/10.1186/s12969-018-0277-2</a>
DOI - Digital Object Identifier
<a href="http://dx.doi.org/10.1186/s12969-018-0277-2" target="_blank" >10.1186/s12969-018-0277-2</a>
Alternative languages
Result language
angličtina
Original language name
Towards a new set of classification criteria for PFAPA syndrome
Original language description
Background: Diagnosis of Periodic Fever, Aphthous stomatitis, Pharyngitis and Cervical Adenitis (PFAPA) syndrome is currently based on the modified Marshall's criteria, but no validated evidence based classification criteria for PFAPA has been established so far. Methods: A multistep process, based on the Delphi and Nominal Group Technique was conducted. After 2 rounds of e mail Delphi survey involving 21 experts in autoinflammation we obtained a list of variables that were discussed in an International Consensus Conference. Variables reaching the 80% of consensus between participants were included in the new classification criteria. In the second phase the new classification criteria and the modified Marshall's criteria were applied on a cohort of 80 pediatric PFAPA patients to compare their performance. Results: The Delphi Survey was sent to 22 participants, 21 accepted to participate. Thirty variables were obtained from the survey and have been discussed at the Consensus Conference. Through the Nominal Group Technique we obtained a new set of classification criteria. These criteria were more restrictive in respect to the modified Marshall's criteria when applied on our cohort of patients. Conclusion: Our work led us to identify a new set of classification criteria for PFAPA syndrome, but they resulted to be too restrictive to be applied in daily clinical practice for the diagnosis of PFAPA.
Czech name
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Czech description
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Classification
Type
J<sub>imp</sub> - Article in a specialist periodical, which is included in the Web of Science database
CEP classification
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OECD FORD branch
30209 - Paediatrics
Result continuities
Project
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Continuities
V - Vyzkumna aktivita podporovana z jinych verejnych zdroju
Others
Publication year
2018
Confidentiality
S - Úplné a pravdivé údaje o projektu nepodléhají ochraně podle zvláštních právních předpisů
Data specific for result type
Name of the periodical
Pediatric Rheumatology
ISSN
1546-0096
e-ISSN
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Volume of the periodical
16
Issue of the periodical within the volume
September
Country of publishing house
US - UNITED STATES
Number of pages
4
Pages from-to
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UT code for WoS article
000445861800001
EID of the result in the Scopus database
2-s2.0-85053670824