Current Treatment of Endolymphatic Sac Tumor of the Temporal Bone
The result's identifiers
Result code in IS VaVaI
<a href="https://www.isvavai.cz/riv?ss=detail&h=RIV%2F00216208%3A11140%2F18%3A10377206" target="_blank" >RIV/00216208:11140/18:10377206 - isvavai.cz</a>
Result on the web
<a href="https://doi.org/10.1007/s12325-018-0730-0" target="_blank" >https://doi.org/10.1007/s12325-018-0730-0</a>
DOI - Digital Object Identifier
<a href="http://dx.doi.org/10.1007/s12325-018-0730-0" target="_blank" >10.1007/s12325-018-0730-0</a>
Alternative languages
Result language
angličtina
Original language name
Current Treatment of Endolymphatic Sac Tumor of the Temporal Bone
Original language description
An endolymphatic sac tumor (ELST) is a rare, indolent but locally aggressive tumor arising in the posterior petrous ridge. Patients present with sensorineural hearing loss and tinnitus. As the tumor progresses, patients may experience vertigo, ataxia, facial nerve paresis, pain and otorrhea. Most patients present in their 4th or 5th decade with a wide age range. Patients with von Hippel-Lindau disease have an increased likelihood of developing ELST. Histologically, ELST is a low-grade adenocarcinoma. As it progresses, it destroys bone and extends into adjacent tissues. The likelihood of regional or distant metastases is remote. The optimal treatment is resection with negative margins. Patients with positive margins, gross residual disease, or unresectable tumor are treated with radiotherapy or radiosurgery. Late recurrences are common, so long follow-up is necessary to assess efficacy. The likelihood of cure depends on tumor extent and is probably in the range of 50-75%.
Czech name
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Czech description
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Classification
Type
J<sub>imp</sub> - Article in a specialist periodical, which is included in the Web of Science database
CEP classification
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OECD FORD branch
30109 - Pathology
Result continuities
Project
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Continuities
I - Institucionalni podpora na dlouhodoby koncepcni rozvoj vyzkumne organizace
Others
Publication year
2018
Confidentiality
S - Úplné a pravdivé údaje o projektu nepodléhají ochraně podle zvláštních právních předpisů
Data specific for result type
Name of the periodical
Advances in Therapy
ISSN
0741-238X
e-ISSN
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Volume of the periodical
35
Issue of the periodical within the volume
7
Country of publishing house
US - UNITED STATES
Number of pages
12
Pages from-to
887-898
UT code for WoS article
000438990000001
EID of the result in the Scopus database
2-s2.0-85048787322