Large-vessel occlusion in a patient with Emery-Dreifuss muscular dystrophy

Result code in IS VaVaI

<a href="https://www.isvavai.cz/riv?ss=detail&h=RIV%2F00216275%3A25520%2F21%3A39918564" target="_blank" >RIV/00216275:25520/21:39918564 - isvavai.cz</a>

Alternative codes found

RIV/00216208:11120/21:43922943

Result on the web

<a href="https://www.csnn.eu/en/journals/czech-and-slovak-neurology-and-neurosurgery/2021-5-5/large-vessel-occlusion-in-a-patient-with-emery-dreifuss-muscular-dystrophy-128688" target="_blank" >https://www.csnn.eu/en/journals/czech-and-slovak-neurology-and-neurosurgery/2021-5-5/large-vessel-occlusion-in-a-patient-with-emery-dreifuss-muscular-dystrophy-128688</a>

DOI - Digital Object Identifier

<a href="http://dx.doi.org/10.48095/cccsnn2021491" target="_blank" >10.48095/cccsnn2021491</a>

Result language

angličtina

Original language name

Large-vessel occlusion in a patient with Emery-Dreifuss muscular dystrophy

Original language description

During the night, about 3 hours after falling asleep, the patient experienced sudden left movement disorder (there were some dystonic movements on the left side observed and described by her husband) along with marked restlessness. The husband called the emergency service and the patient was admitted to the ICU of the stroke center. Stroke due to embolization to the middle cerebral artery (MCA) was dia gnosed. Brain CT revealed, that penumbra was only aff ected to a small extent; ASPECTS (Alberta Stroke Programm Early CT Scale) was 3 points. CTA of the cerebral arteries showed the occlusion of the terminal section of the internal carotid artery (ICA) on the right side (segment C7) with a transition to the M1/MCA segment (10 mm) (Fig. 1). The patient was consulted at a comprehensive stroke center that did not recommend intravenous thrombolysis or mechanical thrombectomy due to the presence of signifi cant and extensive ischemic changes in the brain tissue. The fi nding was evaluated as an emboligenic occlusion of the distal ICA, most likely of cardiac origin. On the next day, somnolence, dysarthria, dysphagia and left-sided hemiplegia were present. A follow-up CT of the brain was performed with the fi nding of expansively behaving ischemia in the right hemisphere with a midline shift, with a subphalcinic and descending transtentorial herniation (Fig. 2). The patient was transferred to neurosurgery, where an extensive right-sided hemicraniectomy was performed. This was followed by a stay at the Anesthesiology and Resuscitation Department. After disconnection from complete mechanical ventilation (immediate postoperative), she was transferred to a neurological ICU. Here, the patient’s environmental cooperation gradually improved, and passive and active rehabilitation was started. The neurological fi nding was dominated by signifi cant psychological changes with fl uctuations in cooperation, partial neglect syndrome, plegia of the left upper limb, and severe paresis of the left lower limb

Czech name

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Czech description

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Type

J_imp - Article in a specialist periodical, which is included in the Web of Science database

CEP classification

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OECD FORD branch

30210 - Clinical neurology

Project

—

Continuities

I - Institucionalni podpora na dlouhodoby koncepcni rozvoj vyzkumne organizace

Publication year

2021

Confidentiality

S - Úplné a pravdivé údaje o projektu nepodléhají ochraně podle zvláštních právních předpisů

Name of the periodical

Česká a slovenská neurologie a neurochirurgie

ISSN

1210-7859

e-ISSN

—

Volume of the periodical

84

Issue of the periodical within the volume

5

Country of publishing house

CZ - CZECH REPUBLIC

Number of pages

2

Pages from-to

491-492

UT code for WoS article

000744166000010

EID of the result in the Scopus database

2-s2.0-85123433825