Giant frontal sinus pneumocele with massive intracranial spread imitating lumboperitoneal shunt malfunction in a predisposed patient with Marfan syndrome

Result code in IS VaVaI
<a href="https://www.isvavai.cz/riv?ss=detail&h=RIV%2F00843989%3A_____%2F19%3AE0107889" target="_blank" >RIV/00843989:_____/19:E0107889 - isvavai.cz</a>
Result on the web
<a href="https://www.csnn.eu/casopisy/ceska-slovenska-neurologie/2019-4-4/objemna-pneumokela-frontalniho-sinu-s-rozsahlym-intrakranialnim-sirenim-imitujicim-dysfunkci-lumboperitonealni-drenaze-u-predisponovaneho-pacienta-s-marfanovym-syndromem-113252/download?hl=cs" target="_blank" >https://www.csnn.eu/casopisy/ceska-slovenska-neurologie/2019-4-4/objemna-pneumokela-frontalniho-sinu-s-rozsahlym-intrakranialnim-sirenim-imitujicim-dysfunkci-lumboperitonealni-drenaze-u-predisponovaneho-pacienta-s-marfanovym-syndromem-113252/download?hl=cs</a>
DOI - Digital Object Identifier
<a href="http://dx.doi.org/10.14735/amcsnn2019458" target="_blank" >10.14735/amcsnn2019458</a>

Result language
angličtina
Original language name
Giant frontal sinus pneumocele with massive intracranial spread imitating lumboperitoneal shunt malfunction in a predisposed patient with Marfan syndrome
Original language description
We report a unique case of giant frontal sinus pneumocele in a predisposed patient with Marfan syndrome. This pneumocele presented potentially life-threatening massive intracranial spread; caused frontal lobe compression, brain midline shift, and lateral ventrikle compression; and imitated lumboperitoneal shunt malfunction. The cause was a fungal infection in the frontal sinus, which obstructed the nasofrontal duct, acting like a unidirectional valve. Development may have been facilitated by the patient’s primary diagnosis of Marfan syndrome associated with skeletal fragility. Although frontal sinus pneumocele spread into the orbit has been described, this is the first reported case with such extensive and potentially life-threatening intracranial spread. We assume that the presence of a lumboperitoneal shunt contributed to this unique occurrence. Despite the huge pneumocele volume, an endoscopic procedure using a combined transnasal and external approach was successful and provided long-term relief.
Czech name
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Czech description
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Type
J<sub>imp</sub> - Article in a specialist periodical, which is included in the Web of Science database
CEP classification
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OECD FORD branch
30206 - Otorhinolaryngology

Project
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Continuities
I - Institucionalni podpora na dlouhodoby koncepcni rozvoj vyzkumne organizace

Publication year
2019
Confidentiality
S - Úplné a pravdivé údaje o projektu nepodléhají ochraně podle zvláštních právních předpisů

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