Fatal Primary Capillary Leak Syndrome in a Late Preterm Newborn

Kód výsledku v IS VaVaI

<a href="https://www.isvavai.cz/riv?ss=detail&h=RIV%2F00064190%3A_____%2F16%3AN0000002" target="_blank" >RIV/00064190:_____/16:N0000002 - isvavai.cz</a>

Nalezeny alternativní kódy

RIV/00216208:11110/16:10328063

Výsledek na webu

<a href="http://dx.doi.org/10.1007/s12098-016-2134-y" target="_blank" >http://dx.doi.org/10.1007/s12098-016-2134-y</a>

DOI - Digital Object Identifier

<a href="http://dx.doi.org/10.1007/s12098-016-2134-y" target="_blank" >10.1007/s12098-016-2134-y</a>

Jazyk výsledku

angličtina

Název v původním jazyce

Fatal Primary Capillary Leak Syndrome in a Late Preterm Newborn

Popis výsledku v původním jazyce

Primary capillary leak syndrome is a rare disease of unknown etiology, characterized by episodes of vascular collapse and plasma extravasation, which may lead to multiple organ failure. Primary capillary leak is extremely rare in children. The authors report a case of a late preterm newborn with fatal capillary leak syndrome of unknown etiology, manifesting as hypotension unresponsive to treatment, extravasation leading to generalised edema, disseminated intravascular coagulation and finally, multiple organ dysfunction syndrome. Aggressive volumotherapy and a combination of inotropes and high doses of terlipressin did not influence systemic vascular collapse and plasma extravasation. The newborn developed multiple organ failure and died on day 27 of life. Investigations performed failed to reveal any specific cause of capillary leak. This is the first report of a fatal primary capillary leak syndrome in a newborn.

Název v anglickém jazyce

Fatal Primary Capillary Leak Syndrome in a Late Preterm Newborn

Popis výsledku anglicky

Primary capillary leak syndrome is a rare disease of unknown etiology, characterized by episodes of vascular collapse and plasma extravasation, which may lead to multiple organ failure. Primary capillary leak is extremely rare in children. The authors report a case of a late preterm newborn with fatal capillary leak syndrome of unknown etiology, manifesting as hypotension unresponsive to treatment, extravasation leading to generalised edema, disseminated intravascular coagulation and finally, multiple organ dysfunction syndrome. Aggressive volumotherapy and a combination of inotropes and high doses of terlipressin did not influence systemic vascular collapse and plasma extravasation. The newborn developed multiple organ failure and died on day 27 of life. Investigations performed failed to reveal any specific cause of capillary leak. This is the first report of a fatal primary capillary leak syndrome in a newborn.

Druh

J_x - Nezařazeno - Článek v odborném periodiku (Jimp, Jsc a Jost)

CEP obor

FG - Pediatrie

OECD FORD obor

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Projekt

—

Návaznosti

V - Vyzkumna aktivita podporovana z jinych verejnych zdroju

Rok uplatnění

2016

Kód důvěrnosti údajů

S - Úplné a pravdivé údaje o projektu nepodléhají ochraně podle zvláštních právních předpisů

Název periodika

INDIAN JOURNAL OF PEDIATRICS

ISSN

0019-5456

e-ISSN

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Svazek periodika

83

Číslo periodika v rámci svazku

10

Stát vydavatele periodika

IN - Indická republika

Počet stran výsledku

2

Strana od-do

1197-199

Kód UT WoS článku

000384813900024

EID výsledku v databázi Scopus

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