Primary ciliary dyskinesia: a consensus statement on diagnostic and treatment approaches in children

Kód výsledku v IS VaVaI

<a href="https://www.isvavai.cz/riv?ss=detail&h=RIV%2F00064203%3A_____%2F09%3A5728" target="_blank" >RIV/00064203:_____/09:5728 - isvavai.cz</a>

Nalezeny alternativní kódy

RIV/00216208:11130/09:5728

Výsledek na webu

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DOI - Digital Object Identifier

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Jazyk výsledku

angličtina

Název v původním jazyce

Primary ciliary dyskinesia: a consensus statement on diagnostic and treatment approaches in children

Popis výsledku v původním jazyce

Primary ciliary dyskinesia (PCD) is associated with abnormal ciliary structure and function, resulting in retention of mucus and bacteria in the respiratory tract, leading to chronic oto-sino-pulmonary disease, situs abnormalities and abnormal sperm motility. The diagnosis of PCD requires presence of the characteristic clinical phenotype and either specific ultrastructural ciliary defects identified by electron microscopy or evidence of abnormal ciliary function. Although the management of children withPCD remains uncertain and evidence is limited, it remains important to follow-up these patients with an adequate and shared care system in order to prevent future lung damage. This ERS consensus statement on the management of children with PCD formulates recommendations for diagnostic and therapeutic approaches with more accurate approach in these patients. Large well-designed randomised controlled trials are required to improve these recommendations.

Název v anglickém jazyce

Primary ciliary dyskinesia: a consensus statement on diagnostic and treatment approaches in children

Popis výsledku anglicky

Primary ciliary dyskinesia (PCD) is associated with abnormal ciliary structure and function, resulting in retention of mucus and bacteria in the respiratory tract, leading to chronic oto-sino-pulmonary disease, situs abnormalities and abnormal sperm motility. The diagnosis of PCD requires presence of the characteristic clinical phenotype and either specific ultrastructural ciliary defects identified by electron microscopy or evidence of abnormal ciliary function. Although the management of children withPCD remains uncertain and evidence is limited, it remains important to follow-up these patients with an adequate and shared care system in order to prevent future lung damage. This ERS consensus statement on the management of children with PCD formulates recommendations for diagnostic and therapeutic approaches with more accurate approach in these patients. Large well-designed randomised controlled trials are required to improve these recommendations.

Druh

J_x - Nezařazeno - Článek v odborném periodiku (Jimp, Jsc a Jost)

CEP obor

FC - Pneumologie

OECD FORD obor

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Projekt

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Návaznosti

Z - Vyzkumny zamer (s odkazem do CEZ)

Rok uplatnění

2009

Kód důvěrnosti údajů

S - Úplné a pravdivé údaje o projektu nepodléhají ochraně podle zvláštních právních předpisů

Název periodika

European Respiratory Journal

ISSN

0903-1936

e-ISSN

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Svazek periodika

34

Číslo periodika v rámci svazku

6

Stát vydavatele periodika

GB - Spojené království Velké Británie a Severního Irska

Počet stran výsledku

13

Strana od-do

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Kód UT WoS článku

000272625000005

EID výsledku v databázi Scopus

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