Unilateral absence of pulmonary artery: Pathophysiology, symptoms, diagnosis and current treatment

Kód výsledku v IS VaVaI

<a href="https://www.isvavai.cz/riv?ss=detail&h=RIV%2F00216224%3A14110%2F13%3A00071659" target="_blank" >RIV/00216224:14110/13:00071659 - isvavai.cz</a>

Nalezeny alternativní kódy

RIV/00159816:_____/13:00060699

Výsledek na webu

<a href="http://dx.doi.org/10.1016/j.acvd.2013.05.004" target="_blank" >http://dx.doi.org/10.1016/j.acvd.2013.05.004</a>

DOI - Digital Object Identifier

<a href="http://dx.doi.org/10.1016/j.acvd.2013.05.004" target="_blank" >10.1016/j.acvd.2013.05.004</a>

Jazyk výsledku

angličtina

Název v původním jazyce

Unilateral absence of pulmonary artery: Pathophysiology, symptoms, diagnosis and current treatment

Popis výsledku v původním jazyce

Unilateral absence of pulmonary artery (UAPA) is a rare malformation that can present as an isolated lesion or may be associated with other congenital heart defects. UAPA is often associated with other congenital cardiovascular anomalies, such as tetralogy of Fallot, atrial septal defect, coarctation of aorta, right aortic arch, truncus arteriosus and pulmonary atresia. Diagnosis of UAPA is very difficult and is based on taking a complete medical history, physical examination and imaging examinations. Clinical symptoms include exercise intolerance, haemoptysis and recurrent respiratory infections. Adult patients with UAPA are often asymptomatic. There is no consensus regarding the treatment for UAPA. The therapeutic approach should be based on symptomsof the patient, pulmonary artery anatomy and associated aortopulmonary collaterals.

Název v anglickém jazyce

Unilateral absence of pulmonary artery: Pathophysiology, symptoms, diagnosis and current treatment

Popis výsledku anglicky

Unilateral absence of pulmonary artery (UAPA) is a rare malformation that can present as an isolated lesion or may be associated with other congenital heart defects. UAPA is often associated with other congenital cardiovascular anomalies, such as tetralogy of Fallot, atrial septal defect, coarctation of aorta, right aortic arch, truncus arteriosus and pulmonary atresia. Diagnosis of UAPA is very difficult and is based on taking a complete medical history, physical examination and imaging examinations. Clinical symptoms include exercise intolerance, haemoptysis and recurrent respiratory infections. Adult patients with UAPA are often asymptomatic. There is no consensus regarding the treatment for UAPA. The therapeutic approach should be based on symptomsof the patient, pulmonary artery anatomy and associated aortopulmonary collaterals.

Druh

J_x - Nezařazeno - Článek v odborném periodiku (Jimp, Jsc a Jost)

CEP obor

FA - Kardiovaskulární nemoci včetně kardiochirurgie

OECD FORD obor

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Projekt

<a href="/cs/project/ED1.100%2F02%2F0123" target="_blank" >ED1.100/02/0123: Fakultní nemocnice u sv. Anny v Brně - Mezinárodní centrum klinického výzkumu (FNUSA - ICRC)</a><br>

Návaznosti

I - Institucionalni podpora na dlouhodoby koncepcni rozvoj vyzkumne organizace

Rok uplatnění

2013

Kód důvěrnosti údajů

S - Úplné a pravdivé údaje o projektu nepodléhají ochraně podle zvláštních právních předpisů

Název periodika

ARCHIVES OF CARDIOVASCULAR DISEASES

ISSN

1875-2136

e-ISSN

—

Svazek periodika

106

Číslo periodika v rámci svazku

8-9

Stát vydavatele periodika

IT - Italská republika

Počet stran výsledku

7

Strana od-do

448-454

Kód UT WoS článku

000324722000005

EID výsledku v databázi Scopus

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