Giant frontal sinus pneumocele with massive intracranial spread imitating lumboperitoneal shunt malfunction in a predisposed patient with Marfan syndrome

Kód výsledku v IS VaVaI

<a href="https://www.isvavai.cz/riv?ss=detail&h=RIV%2F00843989%3A_____%2F19%3AE0107889" target="_blank" >RIV/00843989:_____/19:E0107889 - isvavai.cz</a>

Výsledek na webu

<a href="https://www.csnn.eu/casopisy/ceska-slovenska-neurologie/2019-4-4/objemna-pneumokela-frontalniho-sinu-s-rozsahlym-intrakranialnim-sirenim-imitujicim-dysfunkci-lumboperitonealni-drenaze-u-predisponovaneho-pacienta-s-marfanovym-syndromem-113252/download?hl=cs" target="_blank" >https://www.csnn.eu/casopisy/ceska-slovenska-neurologie/2019-4-4/objemna-pneumokela-frontalniho-sinu-s-rozsahlym-intrakranialnim-sirenim-imitujicim-dysfunkci-lumboperitonealni-drenaze-u-predisponovaneho-pacienta-s-marfanovym-syndromem-113252/download?hl=cs</a>

DOI - Digital Object Identifier

<a href="http://dx.doi.org/10.14735/amcsnn2019458" target="_blank" >10.14735/amcsnn2019458</a>

Jazyk výsledku

angličtina

Název v původním jazyce

Giant frontal sinus pneumocele with massive intracranial spread imitating lumboperitoneal shunt malfunction in a predisposed patient with Marfan syndrome

Popis výsledku v původním jazyce

We report a unique case of giant frontal sinus pneumocele in a predisposed patient with Marfan syndrome. This pneumocele presented potentially life-threatening massive intracranial spread; caused frontal lobe compression, brain midline shift, and lateral ventrikle compression; and imitated lumboperitoneal shunt malfunction. The cause was a fungal infection in the frontal sinus, which obstructed the nasofrontal duct, acting like a unidirectional valve. Development may have been facilitated by the patient’s primary diagnosis of Marfan syndrome associated with skeletal fragility. Although frontal sinus pneumocele spread into the orbit has been described, this is the first reported case with such extensive and potentially life-threatening intracranial spread. We assume that the presence of a lumboperitoneal shunt contributed to this unique occurrence. Despite the huge pneumocele volume, an endoscopic procedure using a combined transnasal and external approach was successful and provided long-term relief.

Název v anglickém jazyce

Giant frontal sinus pneumocele with massive intracranial spread imitating lumboperitoneal shunt malfunction in a predisposed patient with Marfan syndrome

Popis výsledku anglicky

We report a unique case of giant frontal sinus pneumocele in a predisposed patient with Marfan syndrome. This pneumocele presented potentially life-threatening massive intracranial spread; caused frontal lobe compression, brain midline shift, and lateral ventrikle compression; and imitated lumboperitoneal shunt malfunction. The cause was a fungal infection in the frontal sinus, which obstructed the nasofrontal duct, acting like a unidirectional valve. Development may have been facilitated by the patient’s primary diagnosis of Marfan syndrome associated with skeletal fragility. Although frontal sinus pneumocele spread into the orbit has been described, this is the first reported case with such extensive and potentially life-threatening intracranial spread. We assume that the presence of a lumboperitoneal shunt contributed to this unique occurrence. Despite the huge pneumocele volume, an endoscopic procedure using a combined transnasal and external approach was successful and provided long-term relief.

Druh

J_imp - Článek v periodiku v databázi Web of Science

CEP obor

—

OECD FORD obor

30206 - Otorhinolaryngology

Projekt

—

Návaznosti

I - Institucionalni podpora na dlouhodoby koncepcni rozvoj vyzkumne organizace

Rok uplatnění

2019

Kód důvěrnosti údajů

S - Úplné a pravdivé údaje o projektu nepodléhají ochraně podle zvláštních právních předpisů

Název periodika

Česká a slovenská neurologie a neurochirurgie

ISSN

1210-7859

e-ISSN

1802-4041

Svazek periodika

82

Číslo periodika v rámci svazku

4

Stát vydavatele periodika

CZ - Česká republika

Počet stran výsledku

3

Strana od-do

458-460

Kód UT WoS článku

000500970200019

EID výsledku v databázi Scopus

2-s2.0-85071114052