Ebstein's anomaly with significant dysplasia of the tricuspid valve presenting at 73 years of age. A case report

Kód výsledku v IS VaVaI

<a href="https://www.isvavai.cz/riv?ss=detail&h=RIV%2F65269705%3A_____%2F19%3A00070950" target="_blank" >RIV/65269705:_____/19:00070950 - isvavai.cz</a>

Nalezeny alternativní kódy

RIV/00216224:14110/19:00112953

Výsledek na webu

<a href="https://e-coretvasa.cz/pdfs/cor/2019/03/10.pdf" target="_blank" >https://e-coretvasa.cz/pdfs/cor/2019/03/10.pdf</a>

DOI - Digital Object Identifier

<a href="http://dx.doi.org/10.1016/j.crvasa.2018.07.004" target="_blank" >10.1016/j.crvasa.2018.07.004</a>

Jazyk výsledku

angličtina

Název v původním jazyce

Ebstein's anomaly with significant dysplasia of the tricuspid valve presenting at 73 years of age. A case report

Popis výsledku v původním jazyce

Ebstein&apos;s anomaly (EA) is a rare congenital heart defect, characterized by an anomalous tricuspid valve displaced towards the apex of the right ventricle (RV); it is usually accompanied by regurgitation. While its severe forms with an extremely dilated functional RV and oppression of the left heart chambers result in the development of severe heart failure at a young age and, in some cases, even prenatally, patients with mild EA may live until old age with the condition unrecognized. We present the case of a patient with a milder form of EA and a contribution of dysplasia, with the disease undiagnosed until his eighties when he developed heart failure accompanied by significant tricuspid regurgitation. Tricuspid valve replacement with a bioprosthesis and atrial septal defect occlusion were followed by significant improvement of RV function and remission of the patient&apos;s problems.

Název v anglickém jazyce

Ebstein's anomaly with significant dysplasia of the tricuspid valve presenting at 73 years of age. A case report

Popis výsledku anglicky

Ebstein&apos;s anomaly (EA) is a rare congenital heart defect, characterized by an anomalous tricuspid valve displaced towards the apex of the right ventricle (RV); it is usually accompanied by regurgitation. While its severe forms with an extremely dilated functional RV and oppression of the left heart chambers result in the development of severe heart failure at a young age and, in some cases, even prenatally, patients with mild EA may live until old age with the condition unrecognized. We present the case of a patient with a milder form of EA and a contribution of dysplasia, with the disease undiagnosed until his eighties when he developed heart failure accompanied by significant tricuspid regurgitation. Tricuspid valve replacement with a bioprosthesis and atrial septal defect occlusion were followed by significant improvement of RV function and remission of the patient&apos;s problems.

Druh

J_imp - Článek v periodiku v databázi Web of Science

CEP obor

—

OECD FORD obor

30201 - Cardiac and Cardiovascular systems

Projekt

—

Návaznosti

I - Institucionalni podpora na dlouhodoby koncepcni rozvoj vyzkumne organizace

Rok uplatnění

2019

Kód důvěrnosti údajů

S - Úplné a pravdivé údaje o projektu nepodléhají ochraně podle zvláštních právních předpisů

Název periodika

Cor et Vasa

ISSN

0010-8650

e-ISSN

—

Svazek periodika

61

Číslo periodika v rámci svazku

3

Stát vydavatele periodika

NL - Nizozemsko

Počet stran výsledku

4

Strana od-do

314-317

Kód UT WoS článku

000472526800010

EID výsledku v databázi Scopus

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