Idiopathic vs. secondary retroperitoneal fibrosis: a clinicopathological study of 12 cases, with emphasis to possible relationship to IgG4-related disease

Kód výsledku v IS VaVaI

<a href="https://www.isvavai.cz/riv?ss=detail&h=RIV%2F00179906%3A_____%2F13%3A10173407" target="_blank" >RIV/00179906:_____/13:10173407 - isvavai.cz</a>

Nalezeny alternativní kódy

RIV/00216208:11150/13:10173407

Výsledek na webu

<a href="http://download.springer.com/static/pdf/855/art%253A10.1007%252Fs00428-013-1480-7.pdf?auth66=1392201175_27eff28118401c974372fc078e55ee3d&ext=.pdf" target="_blank" >http://download.springer.com/static/pdf/855/art%253A10.1007%252Fs00428-013-1480-7.pdf?auth66=1392201175_27eff28118401c974372fc078e55ee3d&ext=.pdf</a>

DOI - Digital Object Identifier

<a href="http://dx.doi.org/10.1007/s00428-013-1480-7" target="_blank" >10.1007/s00428-013-1480-7</a>

Jazyk výsledku

angličtina

Název v původním jazyce

Idiopathic vs. secondary retroperitoneal fibrosis: a clinicopathological study of 12 cases, with emphasis to possible relationship to IgG4-related disease

Popis výsledku v původním jazyce

Retroperitoneal fibrosis (RF) is a rare disease characterized by inflammation and fibrosis of retroperitoneal soft tissues. It is classified into 2 types: idiopathic (iRF), and secondary (sRF). The aim of the study was to investigate the relationship between iRF and IgG4-related disease (IgG4-RD) and to eventually extend the clinicopathological features of this condition by analysis of the sample comprising 6 iRF- and 6 sRF-patients. The iRF-patients included 4 males and 2 females, aged 12-62 years (median 55 years). Two lesions were periaortic, 1 was periureteral and 3 cases showed both periaortic and periureteral localization. Two patients had increased serum levels of IgG4. None of the patients developed any manifestation of IgG4-RD during the follow-up period ranging for 15 - 133 months (median 43 months). Microscopically, in 2 iRF-cases fibrosis was highly cellular encircling vessels, nerves and paraganglia. Phlebitis was found in all cases being obliterative in 4. Lymphocytic inf

Název v anglickém jazyce

Idiopathic vs. secondary retroperitoneal fibrosis: a clinicopathological study of 12 cases, with emphasis to possible relationship to IgG4-related disease

Popis výsledku anglicky

Retroperitoneal fibrosis (RF) is a rare disease characterized by inflammation and fibrosis of retroperitoneal soft tissues. It is classified into 2 types: idiopathic (iRF), and secondary (sRF). The aim of the study was to investigate the relationship between iRF and IgG4-related disease (IgG4-RD) and to eventually extend the clinicopathological features of this condition by analysis of the sample comprising 6 iRF- and 6 sRF-patients. The iRF-patients included 4 males and 2 females, aged 12-62 years (median 55 years). Two lesions were periaortic, 1 was periureteral and 3 cases showed both periaortic and periureteral localization. Two patients had increased serum levels of IgG4. None of the patients developed any manifestation of IgG4-RD during the follow-up period ranging for 15 - 133 months (median 43 months). Microscopically, in 2 iRF-cases fibrosis was highly cellular encircling vessels, nerves and paraganglia. Phlebitis was found in all cases being obliterative in 4. Lymphocytic inf

Druh

J_x - Nezařazeno - Článek v odborném periodiku (Jimp, Jsc a Jost)

CEP obor

FP - Ostatní lékařské obory

OECD FORD obor

—

Projekt

<a href="/cs/project/LM2010004" target="_blank" >LM2010004: BBMRI_CZ v rámci budování české části velké distribuované výzkumné infrastruktury pan-evropského významu: vytvoření a provoz sítě bank biologického materiálu pro biomedicínský výzkum</a><br>

Návaznosti

I - Institucionalni podpora na dlouhodoby koncepcni rozvoj vyzkumne organizace

Rok uplatnění

2013

Kód důvěrnosti údajů

S - Úplné a pravdivé údaje o projektu nepodléhají ochraně podle zvláštních právních předpisů

Název periodika

Virchows Archiv : an international journal of pathology

ISSN

0945-6317

e-ISSN

—

Svazek periodika

463

Číslo periodika v rámci svazku

5

Stát vydavatele periodika

DE - Spolková republika Německo

Počet stran výsledku

10

Strana od-do

721-730

Kód UT WoS článku

000326929400013

EID výsledku v databázi Scopus

—